An exceptional case of bladder exstrophy with pubic symphysis diastasis in a 3-year-old male child

Bladder exstrophy is a rare birth defect in which the anterior wall of the abdomen over the bladder is not closed in the intrauterine period, hence the child born with exposed bladder. Incidence of bladder exstrophy is 1/10,000 childbirths. Complaints would vary from exposed bladder, incontinence or leakage of urine, defect in genitals and pelvic bones as well as defect in intestine and reproductive organs. Mostly patient get operated with bladder exstrophy repair in infant age. If it gets neglected, it needs stage wise surgery in this case. Parents of a 3-year-old male child came to Paediatric surgeon OPD with congenital bladder exstrophy. Orthopaedic surgeons´ opinion was taken in view of pubic diastasis. In infant age, there is no need of additional concern of pubic diastasis. At age of 3 acetabulo-pelvic surgeon advice for External fixator application if pelvic wings to decrease tension on reconstructed bladder wall and inter-pubic ligament. Patient managed as neglected bladder exstrophy. Reconstruction of abdominal wall and urethra reconstruction done and application of external fixator application done.